1.3.8.6: glutaryl-CoA dehydrogenase (ETF)
This is an abbreviated version!
For detailed information about glutaryl-CoA dehydrogenase (ETF), go to the full flat file.
Word Map on EC 1.3.8.6
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1.3.8.6
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glutaric
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aciduria
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3-hydroxyglutaric
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striatal
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dystonia
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encephalopathic
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ga1
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macrocephaly
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inborn
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neurometabolic
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crises
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glutarylcarnitine
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hydroxylysine
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carnitine
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crotonyl-coa
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glutaconic
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intercurrent
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3-oh-ga
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frontotemporal
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neuroradiological
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acylcarnitine
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excretors
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medicine
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glutaconyl-coa
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acidaemia
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subdural
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isovaleryl-coa
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glutarylation
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sylvian
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pharmacology
- 1.3.8.6
-
glutaric
- aciduria
-
3-hydroxyglutaric
- striatal
- dystonia
-
encephalopathic
- ga1
-
macrocephaly
-
inborn
-
neurometabolic
- crises
-
glutarylcarnitine
- hydroxylysine
- carnitine
- crotonyl-coa
-
glutaconic
-
intercurrent
-
3-oh-ga
-
frontotemporal
-
neuroradiological
- acylcarnitine
-
excretors
- medicine
- glutaconyl-coa
-
acidaemia
-
subdural
- isovaleryl-coa
-
glutarylation
-
sylvian
- pharmacology
Reaction
Synonyms
decarboxylating glutaryl-coenzyme A dehydrogenase, EC 1.3.99.7, GCD, GCDH, GDH, GDHGeo, glutaryl coenzyme A dehydrogenase, glutaryl-CoA dehydrogenase, glutaryl-coenzyme A dehydrogenase, More
ECTree
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KM Value
KM Value on EC 1.3.8.6 - glutaryl-CoA dehydrogenase (ETF)
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0.0004
electron transfer flavoprotein
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recombinant wild-type enzyme, pH 7.6, 25°C
0.0064
glutaryl-CoA
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recombinant wild-type enzyme, pH 7.6, 25°C, electron acceptor is electron transfer flavoprotein
0.0074
glutaryl-CoA
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mutant A421T, pH 7.6, 25°C, electron acceptor is electron transfer flavoprotein
0.0123
glutaryl-CoA
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mutant A421V, pH 7.6, 25°C, electron acceptor is electron transfer flavoprotein
0.02
glutaryl-CoA
recombinant mutant V400M with ETF, pH 7.8, temperature not specified in the publication
0.0211
glutaryl-CoA
recombinant wild-type enzyme with ETF, pH 7.8, temperature not specified in the publication
0.0261
glutaryl-CoA
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mutant A433V, pH 7.6, 25°C, electron acceptor is electron transfer flavoprotein
0.0326
glutaryl-CoA
recombinant mutant R227P with ETF, pH 7.8, temperature not specified in the publication
0.035
glutaryl-CoA
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mutant E370Q, pH and temperature not specified in the publication
0.0481
glutaryl-CoA
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mutant T429M, pH 7.6, 25°C, electron acceptor is electron transfer flavoprotein
3.8
glutaryl-CoA
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wild-type enzyme, pH and temperature not specified in the publication
additional information
additional information
reaction and inhibition kinetics
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additional information
additional information
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reaction and inhibition kinetics
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additional information
additional information
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kinetics with medium chain acyl-CoA substrates, overview
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additional information
additional information
Michaelis-Menten steady-state kinetic analysis for wild-type and mutant enzymes
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additional information
additional information
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Michaelis-Menten steady-state kinetic analysis for wild-type and mutant enzymes
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