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2.4.1.244: N-acetyl-beta-glucosaminyl-glycoprotein 4-beta-N-acetylgalactosaminyltransferase

This is an abbreviated version!
For detailed information about N-acetyl-beta-glucosaminyl-glycoprotein 4-beta-N-acetylgalactosaminyltransferase, go to the full flat file.

Word Map on EC 2.4.1.244

Reaction

UDP-N-acetyl-alpha-D-galactosamine
+
N-acetyl-beta-D-glucosaminyl group
=
UDP
+
N-acetyl-beta-D-galactosaminyl-(1->4)-N-acetyl-beta-D-glucosaminyl group

Synonyms

B4GALNT3, beta 1,4-N-acetylgalactosaminyltransferase-A, beta1,4-N-acetylgalactosaminyltransferase, beta1,4-N-acetylgalactosaminyltransferase II, beta1,4-N-acetylgalactosaminyltransferase III, beta1,4-N-acetylgalactosaminyltransferase IV, beta1,4-N-acetylgalactosaminyltransferase-III, beta4GalNAc-T3, beta4GalNAc-T4, beta4GalNAcT, beta4GalNAcT-II, beta4GalNAcTA, beta4GalNAcTB, N,N'-diacetyllactosediamine synthase, N-acetyl-beta-glucosaminyl-glycoprotein 4-beta-N-acetylgalactosaminyltransferase 1, N-acetyl-beta-glucosaminyl-glycoprotein 4-beta-N-acetylgalactosaminyltransferase 2

ECTree

     2 Transferases
         2.4 Glycosyltransferases
             2.4.1 Hexosyltransferases
                2.4.1.244 N-acetyl-beta-glucosaminyl-glycoprotein 4-beta-N-acetylgalactosaminyltransferase

Systematic Name

Systematic Name on EC 2.4.1.244 - N-acetyl-beta-glucosaminyl-glycoprotein 4-beta-N-acetylgalactosaminyltransferase

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SYSTEMATIC NAME
IUBMB Comments
UDP-N-acetyl-D-galactosamine:N-acetyl-beta-D-glucosaminyl-group 4-beta-N-acetylgalactosaminyltransferase
The enzyme from human can transfer N-acetyl-D-galactosamine (GalNAc) to N-glycan and O-glycan substrates that have N-acetyl-D-glucosamine (GlcNAc) but not D-glucuronic acid (GlcUA) at their non-reducing end. The N-acetyl-beta-D-glucosaminyl group is normally on a core oligosaccharide although benzyl glycosides have been used in enzyme-characterization experiments. Some glycohormones, e.g. lutropin and thyrotropin contain the N-glycan structure containing the N-acetyl-beta-D-galactosaminyl-(1->4)-N-acetyl-beta-D-glucosaminyl group.