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2.4.1.274: glucosylceramide beta-1,4-galactosyltransferase

This is an abbreviated version!
For detailed information about glucosylceramide beta-1,4-galactosyltransferase, go to the full flat file.

Word Map on EC 2.4.1.274

Reaction

UDP-alpha-D-galactose
+
beta-D-glucosyl-(1<->1)-ceramide
=
UDP
+
beta-D-galactosyl-(1->4)-beta-D-glucosyl-(1<->1)-ceramide

Synonyms

B4GalT5, B4GalT6, beta-1,4-galactosyltransferase V, beta-1,4-GalT-V, beta4-galactosyltransferase 5, beta4GalT5, Lac-Cer synthase, LacCer synthase, lactosylceramide synthase, UDP-Ga1:glucosylceramide beta1->4galactosyltransferase, UDP-Gal:glucosylceramide beta-1,4-galactosyltransferase, UDP-galactose:GlcCer, beta1-4 galactosyltransferase, UDPgalactose:glucosylceramide beta1->4-galactosyltransferase

ECTree

     2 Transferases
         2.4 Glycosyltransferases
             2.4.1 Hexosyltransferases
                2.4.1.274 glucosylceramide beta-1,4-galactosyltransferase

Source Tissue

Source Tissue on EC 2.4.1.274 - glucosylceramide beta-1,4-galactosyltransferase

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SOURCE TISSUE
ORGANISM
UNIPROT
COMMENTARY hide
LITERATURE
SOURCE
high expression
Manually annotated by BRENDA team
low axpression
Manually annotated by BRENDA team
isoform beta4GalT5 works predominantly in mouse embryonic fibroblasts
Manually annotated by BRENDA team
low axpression
Manually annotated by BRENDA team
low axpression
Manually annotated by BRENDA team
alveolar mactrophage
Manually annotated by BRENDA team
-
from normal and familial hypercholesterolemic homozygotes. Urinary proximal tubular cells from familial hypercholesterolemic homozygous patients contain glucosylceramide beta-1,4-galactosyltransferase activity 35% higher as compared to control cells
Manually annotated by BRENDA team
additional information