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Literature summary for 1.3.8.7 extracted from

  • Derks, T.G.; Boer, T.S.; van Assen, A.; Bos, T.; Ruiter, J.; Waterham, H.R.; Niezen-Koning, K.E.; Wanders, R.J.; Rondeel, J.M.; Loeber, J.G.; Ten Kate, L.P.; Smit, G.P.; Reijngoud, D.J.
    Neonatal screening for medium-chain acyl-CoA dehydrogenase (MCAD) deficiency in the Netherlands: the importance of enzyme analysis to ascertain true MCAD deficiency (2008), J. Inherit. Metab. Dis., 31, 88-96.
    View publication on PubMed

Localization

Localization Comment Organism GeneOntology No. Textmining
mitochondrion
-
Homo sapiens 5739
-

Organism

Organism UniProt Comment Textmining
Homo sapiens
-
-
-

Source Tissue

Source Tissue Comment Organism Textmining
fibroblast
-
Homo sapiens
-
leukocyte
-
Homo sapiens
-
lymphocyte
-
Homo sapiens
-

Substrates and Products (Substrate)

Substrates Comment Substrates Organism Products Comment (Products) Rev. Reac.
hexanoyl-CoA + acceptor
-
Homo sapiens 2-hexenoyl-CoA + reduced acceptor
-
?
phenylpropionyl-CoA + acceptor
-
Homo sapiens ? + reduced acceptor
-
?

Synonyms

Synonyms Comment Organism
MCAD
-
Homo sapiens