Literature summary for 1.1.3.27 extracted from

Wanders, R.J.A.; van Roermund, C.W.T.; Schor, D.S.M.; ten Brink, H.J.; Jakobs, C.
2-Hydroxyphytanic acid oxidase activity in rat and human liver and its deficiency in the Zellweger syndrome (1994), Biochim. Biophys. Acta, 1227, 177-182.

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Localization

Localization	Comment	Organism	GeneOntology No.	Textmining
peroxisome	-	Homo sapiens	5777	-
peroxisome	-	Rattus norvegicus	5777	-

Natural Substrates/ Products (Substrates)

Natural Substrates	Organism	Comment (Nat. Sub.)	Natural Products	Comment (Nat. Pro.)	Rev.	Reac.
L-2-hydroxyphytanate + O2	Rattus norvegicus	-	2-oxophytanate + H2O2	-	?
L-2-hydroxyphytanate + O2	Homo sapiens	deficiency in patients with Zellweger syndrome, which lack morphologically distinguishable peroxisomes	2-oxophytanate + H2O2	-	?

Organism

Organism	UniProt	Comment	Textmining
Homo sapiens	-	-	-
Rattus norvegicus	-	-	-

Source Tissue

Source Tissue	Comment	Organism	Textmining
liver	-	Homo sapiens	-
liver	-	Rattus norvegicus	-

Substrates and Products (Substrate)

Substrates	Comment Substrates	Organism	Products	Comment (Products)	Rev.	Reac.
L-2-hydroxyphytanate + O2	-	Homo sapiens	2-oxophytanate + H2O2	-	?
L-2-hydroxyphytanate + O2	-	Rattus norvegicus	2-oxophytanate + H2O2	-	?
L-2-hydroxyphytanate + O2	deficiency in patients with Zellweger syndrome, which lack morphologically distinguishable peroxisomes	Homo sapiens	2-oxophytanate + H2O2	-	?

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Release 2023.1 (January 2023)