Metals/Ions | Comment | Organism | Structure |
---|---|---|---|
Iron | required | Homo sapiens |
Organism | UniProt | Comment | Textmining |
---|---|---|---|
Homo sapiens | - |
- |
- |
Source Tissue | Comment | Organism | Textmining |
---|---|---|---|
liver | - |
Homo sapiens | - |
Substrates | Comment Substrates | Organism | Products | Comment (Products) | Rev. | Reac. |
---|---|---|---|---|---|---|
phytanoyl-CoA + 2-oxoglutarate + O2 | 3R and 3S epimers are hydroxylated with approximately equal efficiency. Both unprocessed proenzyme and mature form of PAHX are fully active | Homo sapiens | 2-hydroxyphytanoyl-CoA + succinate + CO2 | - |
? |
Synonyms | Comment | Organism |
---|---|---|
PAHX | - |
Homo sapiens |
phytanoyl-CoA 2-hydroxylase | - |
Homo sapiens |