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Literature summary for 1.14.11.7 extracted from

  • Morello, R.; Bertin, T.K.; Chen, Y.; Hicks, J.; Tonachini, L.; Monticone, M.; Castagnola, P.; Rauch, F.; Glorieux, F.H.; Vranka, J.; Baechinger, H.P.; Pace, J.M.; Schwarze, U.; Byers, P.H.; Weis, M.; Fernandes, R.J.; Eyre, D.R.; Yao, Z.; Boyce, B.F.; Lee, B.
    CRTAP is required for prolyl 3- hydroxylation and mutations cause recessive osteogenesis imperfecta (2006), Cell, 127, 291-304.
    View publication on PubMed

Activating Compound

Activating Compound Comment Organism Structure
cartilage associated protein
-
Mus musculus

Molecular Weight [Da]

Molecular Weight [Da] Molecular Weight Maximum [Da] Comment Organism
51530
-
multi-angle laser-light scattering Mus musculus

Organism

Organism UniProt Comment Textmining
Mus musculus
-
-
-

Purification (Commentary)

Purification (Comment) Organism
-
Mus musculus

Source Tissue

Source Tissue Comment Organism Textmining
bone
-
Mus musculus
-
fibroblast
-
Mus musculus
-
osteoblast
-
Mus musculus
-

Substrates and Products (Substrate)

Substrates Comment Substrates Organism Products Comment (Products) Rev. Reac.
procollagen + 2-oxoglutarate + O2
-
Mus musculus procollagen trans-3-hydroxy-L-proline + succinate + CO2
-
?

Synonyms

Synonyms Comment Organism
P3H1
-
Mus musculus
prolyl 3-hydroxylase 1
-
Mus musculus