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Literature summary for 1.14.18.6 extracted from

  • Eckhardt, M.; Yaghootfam, A.; Fewou, S.; Z๖ller, I.; Gieselmann, V.
    A mammalian fatty acid hydroxylase responsible for the formation of alpha-hydroxylated galactosylceramide in myelin (2005), Biochem. J., 388, 245-254.
    View publication on PubMedView publication on EuropePMC

Cloned(Commentary)

Cloned (Comment) Organism
expression in CHO cells Mus musculus

Localization

Localization Comment Organism GeneOntology No. Textmining
endoplasmic reticulum
-
Mus musculus 5783
-

Molecular Weight [Da]

Molecular Weight [Da] Molecular Weight Maximum [Da] Comment Organism
70000
-
x * 71800, calculated, x * 70000, SDS-PAGE Mus musculus
71800
-
x * 71800, calculated, x * 70000, SDS-PAGE Mus musculus

Organism

Organism UniProt Comment Textmining
Mus musculus Q5MPP0
-
-

Source Tissue

Source Tissue Comment Organism Textmining
brain expression in white matter. Time course of expression in brain closely follows the expression of myelin-specific genes, reaching a maximum at 2-3 weeks of age Mus musculus
-
kidney
-
Mus musculus
-
skin
-
Mus musculus
-
stomach
-
Mus musculus
-
testis
-
Mus musculus
-

Substrates and Products (Substrate)

Substrates Comment Substrates Organism Products Comment (Products) Rev. Reac.
monohexosylceramide + 2 ferrocytochrome b5 + O2 + 2 H+
-
Mus musculus 2'-hydroxymonohexosylceramide + 2 ferricytochrome b5 + H2O
-
?

Subunits

Subunits Comment Organism
? x * 71800, calculated, x * 70000, SDS-PAGE Mus musculus

Synonyms

Synonyms Comment Organism
FA2H
-
Mus musculus
fatty acid 2-hydroxylase
-
Mus musculus

Cofactor

Cofactor Comment Organism Structure
cytochrome b5
-
Mus musculus

General Information

General Information Comment Organism
physiological function transfection of FA2H cDNA in CHO cells leads to the formation of hexosylceramide containing alpha-hydroxylated fatty acid Mus musculus