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Literature summary for 1.3.8.1 extracted from

  • Beattie, S.G.; Goetzman, E.; Conlon, T.; Germain, S.; Walter, G.; Campbell-Thompson, M.; Matern, D.; Vockley, J.; Flotte, T.R.
    Biochemical correction of short-chain acyl-coenzyme A dehydrogenase deficiency after portal vein injection of rAAV8-SCAD (2008), Hum. Gene Ther., 19, 579-588.
    View publication on PubMedView publication on EuropePMC

Localization

Localization Comment Organism GeneOntology No. Textmining
mitochondrion
-
Mus musculus 5739
-

Molecular Weight [Da]

Molecular Weight [Da] Molecular Weight Maximum [Da] Comment Organism
41000
-
mature enzyme, SDS-PAGE Mus musculus
44000
-
precursor protein, SDS-PAGE Mus musculus

Organism

Organism UniProt Comment Textmining
Mus musculus
-
-
-

Source Tissue

Source Tissue Comment Organism Textmining
liver
-
Mus musculus
-

Specific Activity [micromol/min/mg]

Specific Activity Minimum [µmol/min/mg] Specific Activity Maximum [µmol/min/mg] Comment Organism
0.0329
-
wild type enzyme Mus musculus

Substrates and Products (Substrate)

Substrates Comment Substrates Organism Products Comment (Products) Rev. Reac.
butyryl-CoA + electron-transferring flavoprotein
-
Mus musculus 2-butenoyl-CoA + reduced electron-transferring flavoprotein
-
?

Synonyms

Synonyms Comment Organism
SCAD
-
Mus musculus
short-chain acyl-coenzyme A dehydrogenase ambiguous Mus musculus