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Literature summary for 1.5.3.7 extracted from

  • Posset, R.; Opp, S.; Struys, E.A.; Voelkl, A.; Mohr, H.; Hoffmann, G.F.; Koelker, S.; Sauer, S.W.; Okun, J.G.
    Understanding cerebral L-lysine metabolism the role of L-pipecolate metabolism in Gcdh-deficient mice as a model for glutaric aciduria type I (2015), J. Inherit. Metab. Dis., 38, 265-272 .
    View publication on PubMed

Localization

Localization Comment Organism GeneOntology No. Textmining
peroxisome
-
Mus musculus 5777
-

Natural Substrates/ Products (Substrates)

Natural Substrates Organism Comment (Nat. Sub.) Natural Products Comment (Nat. Pro.) Rev. Reac.
L-pipecolate + O2 Mus musculus
-
DELTA1-piperideine-6-carboxylate + H2O2
-
?

Organism

Organism UniProt Comment Textmining
Mus musculus
-
-
-

Source Tissue

Source Tissue Comment Organism Textmining
brain
-
Mus musculus
-
additional information not detected in liver Mus musculus
-

Substrates and Products (Substrate)

Substrates Comment Substrates Organism Products Comment (Products) Rev. Reac.
L-pipecolate + O2
-
Mus musculus DELTA1-piperideine-6-carboxylate + H2O2
-
?

Synonyms

Synonyms Comment Organism
L-pipecolate oxidase
-
Mus musculus
L-PIPOX
-
Mus musculus