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Literature summary for 2.7.1.40 extracted from

  • van Oirschot, B.A.; Francois, J.J.; van Solinge, W.W.; van Wesel, A.C.; Rijksen, G.; van Amstel, H.K.; van Wijk, R.
    Novel type of red blood cell pyruvate kinase hyperactivity predicts a remote regulatory locus involved in PKLR gene expression (2014), Am. J. Hematol., 89, 380-384.
    View publication on PubMed

Natural Substrates/ Products (Substrates)

Natural Substrates Organism Comment (Nat. Sub.) Natural Products Comment (Nat. Pro.) Rev. Reac.
ATP + pyruvate Homo sapiens
-
ADP + phosphoenolpyruvate
-
?

Organism

Organism UniProt Comment Textmining
Homo sapiens
-
-
-

Source Tissue

Source Tissue Comment Organism Textmining
erythrocyte
-
Homo sapiens
-

Substrates and Products (Substrate)

Substrates Comment Substrates Organism Products Comment (Products) Rev. Reac.
ATP + pyruvate
-
Homo sapiens ADP + phosphoenolpyruvate
-
?

Synonyms

Synonyms Comment Organism
PK-R
-
Homo sapiens

General Information

General Information Comment Organism
malfunction hereditary enzyme deficiency leads to chronic nonspherocytic hemolytic anemia Homo sapiens
metabolism red blood cell pyruvate kinase is a key regulatory enzyme of red cell metabolism Homo sapiens