Application | Comment | Organism |
---|---|---|
medicine | plasma biotinidase activity assay for diagnosis and screen newborn infants for biotinidase deficiency, treatment of inborn metabolism errors with large doses of biotin | Homo sapiens |
Inhibitors | Comment | Organism | Structure |
---|---|---|---|
iodoacetamide | - |
Homo sapiens | |
phenylmethylsulfonyl fluoride | phenylmethanesulfonamide | Homo sapiens |
KM Value [mM] | KM Value Maximum [mM] | Substrate | Comment | Organism | Structure |
---|---|---|---|---|---|
0.005 | - |
epsilon-N-biotinyl-L-lysine | human serum | Homo sapiens | |
0.0062 | - |
epsilon-N-biotinyl-L-lysine | - |
Homo sapiens | |
0.00625 | - |
epsilon-N-biotinyl-L-lysine | - |
Homo sapiens | |
0.0065 | - |
epsilon-N-biotinyl-L-lysine | - |
Homo sapiens |
Molecular Weight [Da] | Molecular Weight Maximum [Da] | Comment | Organism |
---|---|---|---|
76000 | - |
gel filtration | Homo sapiens |
78000 | - |
gel filtration | Homo sapiens |
115000 | - |
gel filtration, impure biotinidase | Homo sapiens |
Natural Substrates | Organism | Comment (Nat. Sub.) | Natural Products | Comment (Nat. Pro.) | Rev. | Reac. |
---|---|---|---|---|---|---|
biotin amide + H2O | Enterococcus faecalis | - |
? | - |
? | |
biotin amide + H2O | Homo sapiens | very short biotinyl peptides, enzyme is not active when biotin is attached to large native proteins, for example intact holocarboxylases | ? | - |
? | |
epsilon-N-biotinyl-L-lysine + H2O | Homo sapiens | - |
? | - |
? | |
epsilon-N-biotinyl-L-lysine + H2O | Enterococcus faecalis | - |
? | - |
? |
Organism | UniProt | Comment | Textmining |
---|---|---|---|
Enterococcus faecalis | - |
- |
- |
Homo sapiens | - |
human | - |
Purification (Comment) | Organism |
---|---|
- |
Homo sapiens |
Source Tissue | Comment | Organism | Textmining |
---|---|---|---|
blood | serum, plasma, leukocytes | Homo sapiens | - |
liver | - |
Homo sapiens | - |
Substrates | Comment Substrates | Organism | Products | Comment (Products) | Rev. | Reac. |
---|---|---|---|---|---|---|
biotin amide + H2O | - |
Enterococcus faecalis | ? | - |
? | |
biotin amide + H2O | very short biotinyl peptides, enzyme is not active when biotin is attached to large native proteins, for example intact holocarboxylases | Homo sapiens | ? | - |
? | |
epsilon-N-biotinyl-L-lysine + H2O | - |
Homo sapiens | biotin + L-lysine | - |
ir | |
epsilon-N-biotinyl-L-lysine + H2O | - |
Enterococcus faecalis | biotin + L-lysine | - |
ir | |
epsilon-N-biotinyl-L-lysine + H2O | - |
Homo sapiens | ? | - |
? | |
epsilon-N-biotinyl-L-lysine + H2O | - |
Enterococcus faecalis | ? | - |
? | |
p-(N-biotinylamino)benzoic acid + H2O | - |
Enterococcus faecalis | biotin + p-aminobenzoic acid | - |
ir | |
p-(N-biotinylamino)benzoic acid + H2O | PAB, artificial substrate | Homo sapiens | biotin + p-aminobenzoic acid | - |
ir |
Subunits | Comment | Organism |
---|---|---|
monomer | 1 * 76000, SDS-PAGE | Homo sapiens |