1.3.8.4: isovaleryl-CoA dehydrogenase
This is an abbreviated version!
For detailed information about isovaleryl-CoA dehydrogenase, go to the full flat file.
Word Map on EC 1.3.8.4
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1.3.8.4
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acidemia
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acyl-coa
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inborn
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3-methylcrotonyl-coa
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isovalerylglycine
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medium-chain
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lethargy
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flavoenzyme
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isobutyryl-coa
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acylcarnitine
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isovalerylcarnitine
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flavoprotein:ubiquinone
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glutaryl-coa
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2-methylbutyryl-coa
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3-hydroxyisovaleric
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octanoyl-coa
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sweaty
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diagnostics
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medicine
- 1.3.8.4
-
acidemia
- acyl-coa
-
inborn
- 3-methylcrotonyl-coa
-
isovalerylglycine
-
medium-chain
-
lethargy
-
flavoenzyme
- isobutyryl-coa
- acylcarnitine
- isovalerylcarnitine
-
flavoprotein:ubiquinone
- glutaryl-coa
- 2-methylbutyryl-coa
-
3-hydroxyisovaleric
- octanoyl-coa
-
sweaty
- diagnostics
- medicine
Reaction
Synonyms
acyl-CoA dehydrogenase, EC 1.3.99.10, i3VD, iso(3)valeryl-CoA dehydrogenase, isovaleric-CoA dehydrogenase, isovaleroyl-coenzyme A dehydrogenase, isovaleryl-coenzyme A dehydrogenase, IVD, IVDH, LiuA, Pden_3633, SBCAD, short/branched chain acyl-CoA dehydrogenase
ECTree
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Renatured
Renatured on EC 1.3.8.4 - isovaleryl-CoA dehydrogenase
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the recombinant IVDH enzyme mutant E246Q is obtained as an apoprotein, the protein is fully reconstituted to the holoprotein by incubation with flavin adenine dinucleotide (FAD) at a ratio 1:20 (IVDH: FAD) molar excess. The reconstituted E246Q IVDH has no activity for isovaleryl-CoA